Faʻatapulaʻa cardiomyopathy

Faʻatapulaʻa cardiomyopathy e faʻasino i se seti o suiga i le auala e galue ai le maso maso. O nei suiga mafua ai le fatu e faʻatumu le lelei (sili atu taatele) pe oomi mama (le faʻaititia). O isi taimi, e i ai uma faʻafitauli.

I le tulaga o le faʻatapulaʻaina cardiomyopathy, o le fatu fatu o le masani masani lapoʻa pe faʻalauteleina. O le tele o taimi, e masani foi ona pamu. Peitai, e le malolo masani i le taimi i le va o fatu fatu pe a toe foʻi le toto mai le tino (diastole).

E ui lava o le faʻafitauli autu o le le faʻatumuina o le fatu, ae atonu e le pamuina malosi le fatu pe a tupu le faʻamaʻi. Ole faʻagaioiga ole fatu e mafai ona afaina ai mama, ate, ma isi tino. O le faʻatapulaʻaina ole cardiomyopathy e ono aʻafia ai se tasi poʻo le lua foi o potu pito i lalo o le fatu (ventricles). O le taofiofia o le cardiomyopathy o se tulaga e seasea tupu. O mafuaʻaga masani ole amyloidosis ma le maʻila ole fatu ile mea le iloa. E mafai foi ona tupu pe a uma se taotoga o le fatu.

Isi mafuaʻaga o le faʻatapulaʻaina cardiomyopathy aofia ai:

• Amyloidosis fatu
• Carcinoid fatu faʻamaʻi
• Faamai o le fatu ufiufi (endocardium), pei o endomyocardial fibrosis ma Loeffler syndrome (seasea)
• Uʻamea tele (hemochromatosis)
• Sarcoidosis
• Faʻailogaina pe a maeʻa le radiation poʻo le chemotherapy
• Scleroderma
• Tumua o le fatu

Faʻailoga o le fatu faʻaletonu e sili ona taatele. O nei faʻailoga e masani ona atiaʻe lemu i le alu o le taimi.Peitaʻi, o faʻailoga i nisi taimi e amata faʻafuaseʻi ma e ogaoga.

Faʻailoga masani o:

• Mama
• Manava manava e tupu i le po, ma gaioiga po o pe a taoto mafolafola
• Le lelava ma le mafai ona faʻamalositino
• Leai o le fiaai
• Fula o le manava
• Fula o vae ma tapuvae
• Pepe e le tusa pe vave foi

O isi faʻailoga e mafai ona aofia ai:

• Tiga o le fatafata
• Le mafai ona mafaufau loloto
• Galue mimi maualalo
• Manaʻomia urination i le po (i tagata matutua)

E ono faʻaalia se suʻega faʻaletino:

• Faʻateleina (faʻaletonu) pe faʻafefeteina uaua ua
• Faʻateleina le ate
• Lolo crackles ma le masani ai pe mamao le fatu fatu i le fatafata faʻalogo e ala i le stethoscope
• Fluid backup i lima ma vae
• Faailoga o le fatu toilalo

Suʻega mo le faʻatapulaʻaina ole cardiomyopathy aofia ai:

• Cardiac catheterization ma coronary angiography
• Suʻega o le fatafata CT
• Fatafata x-ray
• ECG (electrocardiogram)
• Echocardiogram ma Doppler suesuega
• MRI o le fatu
• Nuclear heart scan (MUGA, RNV)
• Suesuega uʻamea
• Serum ma miaga porotini suʻega

Faʻatonutonu cardiomyopathy ono foliga tutusa ma constrictive pericarditis. E mafai ona fesoasoani le faʻapipiʻi i le fatu fatu e faʻamaonia ai le faʻamaoniga. E seasea lava, o se biopsy o le fatu atonu e manaʻomia.

O le tulaga mafua ai le cardiomyopathy e togafitia pe a mafai ona maua.

E toaitiiti togafitiga e iloa lelei le galue mo le faasaina cardiomyopathy. O le faʻamoemoe autu o togafitiga o le faʻatonutonuina o faʻailoga ma faʻaleleia le tulaga o le olaga.

O togafitiga nei e mafai ona faʻaaoga e faʻatonutonu ai faʻailoga pe puipuia ai faʻafitauli:

• Toto e faʻalaʻitiitiina ai le toto
• Chemotherapy (i nisi tulaga)
• Diuretics e aveʻese vai ma fesoasoani faʻalelei manava
• Vailaau e puipuia pe taofi ai le masani ai fatu fatu
• Steroids poʻo chemotherapy mo nisi mafuaʻaga

E mafai ona iloiloina se taotoga o le fatu pe a fai o le fatu e leaga tele ma e ogaoga faʻailoga.

Tagata e iai lenei faʻalavelave e masani ona tupu ai le faaletonu ole fatu lea e atili ai ona leaga. Faʻafitauli i le fatu fatu poʻo "leaky" fatu faʻamau faʻapitoa mafai foi ona tupu.

Tagata e iai faʻatapulaʻa cardiomyopathy ono avea ma sui filifilia o le fatu. O le vaʻai mamao e faʻamoemoe i le mafuaʻaga o le tulaga, ae e masani ona mativa. Faʻaolaina pe a maeʻa faʻamaoniga ono sili atu ma le 10 tausaga.

Valaʻau i lau fomaʻi pe a fai o loʻo ia oe ni faʻailoga o le faʻatapulaʻaina o le fatu.

Cardiomyopathy - faʻatapulaʻaina; Infiltrative cardiomyopathy; Idiopathic myocardial fibrosis

• Loto - vaega e oʻo i le ogatotonu
• Loto - vaʻai i luma

Falk RH, Hershberger RE. O le lautele, faʻatapulaʻaina, ma infiltrative cardiomyopathies. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald's Heart Disease: O Se Tusitusiga o Faʻafomaʻi Cardiovascular. 11th lomiga. Filatelefia, PA: Elsevier; 2019: chap 77.

McKenna WJ, Elliott PM. Faamai o le myocardium ma le endocardium. I totonu: Goldman L, Schafer AI, eds. Faʻafomaʻi Goldman-Cecil. 26th lomiga. Filatelefia, PA: Elsevier; 2020: mata 54.