Totoina amyloidosis

Hereditary amyloidosis o se tuutuuga lea e le masani ai le teuina o protein (taʻua o le amyloid) i soʻo se tino i le tino. E masani ona faʻaputuputu ni manuʻa leaga i le fatu, fatugaʻo ma le neula. O nei polotini tupe teu e faʻaleagaina le tino ma faʻalavelave i le faʻaogaina o totoga.
Hereditary amyloidosis ua pasi mai i matua i a latou fanau (tofi). E mafai foi ona faia e Genes se sao i le muamua amyloidosis.
Isi ituaiga o amyloidosis e le tuufaasolo mai. E aofia ai:
- Senile systemic: vaʻaia i tagata matutua atu i le 70
- Fuafua: e tupu e aunoa ma se lauiloa mafuaʻaga
- Maualuga: iʻuga mai faʻamaʻi e pei o kanesa o sela toto (myeloma)
Aiaiga faʻapitoa e aofia ai:
- Amyloidosis fatu
- Cerebral amyloidosis
- Amyloidosis faiga faʻalua
Togafitiga e faaleleia ai le gaioiga o faaleagaina totoga o le a fesoasoani faamama avega nisi o faʻailoga o le tupuaga amyloidosis. E mafai ona aoga le toe tui ole ate e faʻaititia ai le fausiaina o polotiniʻi amyloid leaga. Talanoa i lau soifua maloloina e uiga i togafitiga.
Amyloidosis - tupuʻaga; Amyloidosis aiga
Amyloidosis o tamailima
Budd RC, Seldin DC. Amyloidosis. I totonu: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Kelley ma Firestein's Tusitusiga o Rheumatology. 10 ed. Filatelefia, PA: Elsevier; 2017: mata 116.
Gertz MA. Amyloidosis. I totonu: Goldman L, Schafer AI, eds. Faʻafomaʻi Goldman-Cecil. 26th lomiga. Filatelefia, PA: Elsevier; 2020: mata 179
Hawkins PN. Amyloidosis. I: Hochberg MC, Gravallese EM, Silman AJ, Smolen JS, Weinblatt ME, Weisman MH, eds. Rheumatology. 7th ed. Filatelefia, PA: Elsevier; 2019: chap 177