IgA vasculitis - Henoch-Schönlein purpura

IgA vasculitis o se faʻamaʻi e aafia ai lanu viole i luga o le paʻu, soʻoga tiga, gastrointestinal faʻafitauli, ma le glomerulonephritis (o se ituaiga o faʻamaʻi fatu). E lauiloa foʻi ole Henoch-Schönlein purpura (HSP).

IgA vasculitis e mafua mai i se le masani ai tali atu o le puipuiga faiga. O le iʻuga o le fulafula i alava toto toto i le paʻu. E mafai foi ona afaina ia alatoto ile soʻoga, fatugaʻo, poʻo le manava. E le o mautinoa pe aisea ua tupu ai lenei mea.

O le faʻamaʻi e tele na vaʻaia i tamaiti i le va o tausaga 3 ma le 15 tausaga, ae e mafai ona vaaia i tagata matutua. E taatele i tama nai lo teine. Ole tele o tagata na maua ile faʻamaʻi lea na maua ile siama ole respiratory respiratory i vaiaso ua tuanaʻi.

Faʻailoga ma foliga o IgA vasculitis ono aofia ai:

• Lulu viole i luga o le paʻu (purpura). E tupu lenei mea i le toeititi o tamaiti uma ei ai le faʻamaʻi. O lenei mea e masani ona tupu i luga o papa, vae maualalo, ma tulilima.
• Tiga o le manava.
• Tiga soʻoga.
• Le masani le miaga (atonu e leai ni faʻailoga).
• Manava tatā, o nisi taimi e tafetoto.
• Hives poʻo angioedema.
• Faanoi ma puaʻi.
• Fulafula ma le tiga i le scrotum o tama.
• Tigā ulu.

O le tausi soifua maloloina o le a vaʻai i lou tino ma vaʻai i lou paʻu. O le suʻega faʻaletino o le a faʻaalia ai le paʻu o le paʻu (purpura, faʻamaʻa) ma le soʻoga faʻatasi.

O suʻega e mafai ona aofia ai:

• Urinalysis tatau ona faia i tulaga uma.
• Faitau atoa le toto. O le pesi mafai ono masani.
• Suʻega faʻapitoa: o nei mea e tatau ona masani ai.
• Paʻu biopsy, aemaise i tagata matutua.
• Toto suʻega e vaʻai mo isi mafuaʻaga o le fula toto pupula, pei o systemic lupus erythematosus, ANCA-fesoʻotaʻi vasculitis po o le hepatitis.
• I tagata matutua, o se fatugaʻo biopsy tatau ona faia.
• Faʻataʻitaʻiga faʻataʻitaʻiga ole manava peʻa iai le tiga.

E leai se faʻapitoa togafitiga. Ole tele o mataupu e alu lava latou. E mafai ona faʻaleleia le tiga soʻofaʻatasi ma NSAID pei ole naproxen. Afai e le alu ese auga, oe mafai ona faatonuina se vailaʻau e pei o le prednisone.

O le faʻamaʻi e masani lava ona sili atu naʻo ia lava. Lua vaetolu o tamaiti ma IgA vasculitis e naʻo le tasi le vaega. Tasi tasi vaetolu o tamaiti e tele a latou vaega. E tatau i tagata ona i ai se vavalalata fomaʻi tulitatao mo le 6 masina pe a maeʻa vaega e vaʻai ai mo faʻailoga o faʻamaʻi fatugao. Tagata matutua maua se sili atu lamatiaga o le atiaʻe faaumiumi faamaʻi fatugao.

Faʻafitauli e ono aofia ai:

• Toto i totonu o le tino
• Poloka o le manava (i tamaiti)
  
• Faʻafitauli o fatugaʻo (i ni tulaga e seasea tupu)

Valaʻau lau tautua pe a fai:

• Oe atiaʻe faʻailoga o IgA vasculitis, ma latou tumau mo le sili atu i ni nai aso.
• E i ai lau fiva miʻamea poʻo le maualalo o galuega mimi pe a maeʻa se vaega.

Immunoglobulin O le vasculitis; Leukocytoclastic vasculitis; Henoch-Schönlein purpura; HSP

• Henoch-Schonlein purpura i lalo vae
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura i luga o le vae o se pepe
• Henoch-Schonlein purpura i luga o vae o se pepe
• Henoch-Schonlein purpura i luga o vae o se pepe
• Henoch-Schonlein purpura i luga o vae

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Sunderkötter CH, Zelger B, Chen KR, et al. Nomenclature o cutaneous vasculitis: Dermatologic faʻaopoopoga i le 2012 toe iloiloina International Chapel Hill Consensus Conference Nomenclature o Vasculitides. Gugu Rheumatol. 2018; 70 (2): 171-184. PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340.