Tusitala: Charles Brown
Aso O Foafoaga: 6 Fepuari 2021
Faafouga Aso: 24 Apelila 2025
Anonim
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Anotusi

Caroli Syndrome o se seasea ma tupuaga faʻamaʻi e afaina ai le ate, lea na mauaina lona igoa aua o le Farani fomaʻi Jacques Caroli na mauaina ia i le 1958. O se faʻamaʻi iloga e le dilation o auala o loʻo feaveaʻi gaʻo, mafua ai tiga ona o mumu na lava auala e tasi. E mafai ona gaosia cyst ma siama, i le faʻaopopoina i le fesoʻotaʻi ma congenital ate fibrosis, o se sili atu ogaoga ituaiga o faʻamaʻi.

Faʻailoga o Caroli Syndrome

O lenei faʻamaʻi e mafai ona tumau e aunoa ma le faʻaalia o ni faʻailoga mo le sili atu i le 20 tausaga, ae a amata loa ona aliaʻe, e mafai ona avea:

  • Tiga i le itu taumatau o le manava;
  • Fiva;
  • Mu lautele;
  • Tuputupu aʻe;
  • Paʻu samasama ma mata.

O lenei faʻamaʻi e mafai ona aliali mai i soʻo se taimi o le olaga ma ono aʻafia ai ni isi o le aiga, peitaʻi e toe tuʻufaʻatasia, o lona uiga e tatau ona ave uma le tama ma le tina i le fesuiaiga o gafa mo le tamaititi e fanau mai ma lenei faʻamaʻi, o le mea lea e seasea tupu ai.


O le faʻamaoniga e mafai ona faia e ala i le faia o suʻega e faʻaalia ai saccular dilations o le sela uaua gaʻo, e pei o le manava ultrasound, fuafuaina tomography, endoscopic retrograde cholangiopancreatography ma percutaneous transcholaryngeal cholangiography.

Togafitiga mo Caroli Syndrome

Togafitiga aofia ai le tagofia o vailaʻau, taotoga e aveʻese ai le kosi pe a fai o le faʻamaʻi e aʻafia na o le tasi le paʻu o le ate, ma le ate toto atonu e manaʻomia i nisi tulaga. E masani lava, o se tagata e manaʻomia le mulimuli i fomaʻi mo le ola pe a maeʻa faʻamaoniga.

Ina ia faʻaleleia le olaga o le tagata, e fautuaina le mulimuli i ai o le nutristist ina ia mafai ai ona fetuʻunaʻi le taumafataga, ma aloese mai le taumafaina o meaʻai e manaʻomia le tele o le malosi mai le ate, lea e tamaoaiga i mea oona ma mauoa i gaʻo.

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