Wiskott-Aldrich syndrome

Anotusi

• Faʻailoga o Wiskott-Aldrich Syndrome
• Togafitiga mo Wiskott-Aldrich Syndrome

Wiskott-Aldrich syndrome o se faʻamaʻi o le kenera, e faʻaleagaina ai le puipuiga o le tino e aofia ai le T ma le B limafositia, ma sela o le toto e fesoasoani e taofiofia le palapala toto, papalafa.

Faʻailoga o Wiskott-Aldrich Syndrome

Faʻailoga o le wiskott-Aldrich syndrome mafai ona:

Faʻaletonu i le toto:

• Faʻaititia numera ma lapoʻa o lapisi i le toto;
• Cutaneous hemorrhages faʻamatalaina e mumu-lanumoana togitogi le tele o le pine ulu, valaʻauina "petechiae", pe latou te ono lapoʻa ma pei o unooa;
• Toto i luga o le toto (aemaise lava ile taimi ole tamaititi), o nifo toto ma nifoloa umi.

O faʻamaʻi masani e mafua mai i ituaiga uma o meaola niniʻi pei ole:

• Ala o faasalalauga Otitis, sinusitis, niumonia;
• Meningitis, niumonia mafua mai i le Pneumocystis jiroveci;
• Siama siama paʻu mafua mai molluscum contagiosum.

Eczema:

• Tele faʻamaʻi pipisi o le paʻu;
• Paʻu pogisa i luga o le paʻu.

Faʻaaliga taʻutaʻua:

• Vasculitis;
• Hemolytic anemia;
• Idiopathic thrombocytopenic purpura.

O le faʻamaʻi mo lenei faʻamaʻi e mafai ona faia e le fomaʻi o tamaiti pe a maeʻa ona vaʻai totoʻaina faʻailoga ma faʻapitoa suʻega. O le iloiloina o le tele o peleti o se tasi lea o auala e faʻamaonia ai le faʻamaʻi, ona o nai faʻamaʻi e i ai lenei uiga.

Togafitiga mo Wiskott-Aldrich Syndrome

O le togafitiga sili ona talafeagai mo Wiskott-Aldrich syndrome o le tafe o ponaivi ponaivi. O isi ituaiga togafitiga o le aveʻesega o leveleve, aua o lenei okeni faʻaleagaina le laʻititi o lapisi o loʻo iai tagata ma lenei faʻamaʻi, o le faʻaogaina o le hemoglobin ma le faʻaaogaina o vailaʻau faʻafomaʻi.

Ole olaga mo tagata e maua ile faʻamaʻi lenei e maulalo, o e e ola peʻa atoa le sefulu o tausaga e masani lava ona maua ile tuma e pei ole lymphoma ma leukemia.