Fuafua a le Retroperitoneal

O le Retroperitoneal fibrosis o se faʻaletonu o le gasegase e poloka ai paipa (ureter) e aveina le miaga mai fatugaʻo i le afifi.

E tupu le fibrosis ole retretritoneal pe a fai o ni meaola lapopoʻa e faia i le vaega i tua ole manava ma gaʻo. O le aano e fausia ai se vaega tele (poʻo le tele) pe faigata fibrotic aʻa. E mafai ona poloka ai paipa ia e feaveaʻi le miaga mai le fatugaʻo i le tagāmimi.

O le mafuaʻaga o lenei faʻafitauli e tele lava ina le iloa. E taatele i tagata e mai le 40 i le 60 tausaga le matutua. O aliʻi e faʻalua ona tupu aʻe i le tulaga o fafine.

Vave auga:

• Paʻu tiga i le manava e faʻateleina i le taimi
• Tiga ma suiga o lanu i vae (ona o le faʻaititia o le toto tafe)
• Fula o le tasi vae

Faʻailoga mulimuli ane:

• Faʻaitiitia le gaʻo o le urine
• Leai se kesi galuega faatino (anuria)
• Nua, puaʻi, suiga i le mafaufau tulaga mafua mai i fatugaʻo toilalo ma le fausiaina-o oona vailaʻau i le toto
• Ogaoga tiga o le manava ma le toto i le nofoa (ona o le oti o le manava sela)

Abdominal CT scan o le auala sili lea e maua ai se tua o tua.

O isi suʻega e mafai ona fesoasoani e faʻailoaina lenei tulaga aofia ai:

• Suʻesuʻe ma foafoa toto tisaini
• Intravenous pyelogram (IVP), e le pei ona masani ona faʻaaogaina
• Ultrasound fatugaʻo
• MRI o le manava
• CAT vaʻai i le manava ma retroperitoneum

E mafai foi ona faia se biopsy ole vaega tele e faateʻa ai le kanesa.

Corticosteroids e faʻataʻitaʻia muamua. O nisi fomaʻi tausi soifua faʻatonuina foi se vailaʻau e taʻua o le tamoxifen.

Afai e le aoga togafitiga o le corticosteroid, e tatau ona faia se biopsy e faʻamaonia ai le faʻamaoniga. O isi vailaʻau e tineia ai le immune system e mafai ona faatonuina.

A le aoga vailaʻau, e manaʻomia se taotoga ma stent (faʻamamaina o paipa).

O le vaʻaiga e faʻamoemoe i le tele o le faʻafitauli ma le aofaʻi o le faʻaleagaina o fatugaʻo.

O le faʻaleagaina fatugaʻo mafai ona tumau pe tumau.

O le faʻaletonu e ono taitai atu ai i:

• Faʻaauau poloka o paipa e tau mai le fatugaʻo i le tasi poʻo le lua itu
• Paʻu fatugaʻo

Valaʻau lau tautua pe a fai e maualalo lou manava poʻo le itu o le tiga ma laititi le alu o le mimi.

Taumafai e aloese mai le umi faʻaaogaina o vailaʻau e iai methysergide. O lenei vailaʻau ua faʻaalia e mafua ai retroperitoneal fibrosis. Methysergide e masani ona faʻaogaina e togafiti ai le ulu o le ulu.

Idiopathic retroperitoneal fibrosis; Faamaʻi o Ormond

• Lalolagi urinary faiga

Comperat E, Bonsib SM, Cheng L. Renal pelvis ma ureter. I: Cheng L, MacLennan GT, kertwick DG, eds. Urologic Faʻapitoa taotoga. 4th ed. Filatelefia, PA: Elsevier; 2020: mata 3

Nakada SY, Sili SL. Faʻatonutonuina o vaega pito i luga o faʻalavelave o le urinary tract. I le: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, eds. Campbell-Walsh Urology. 11th lomiga. Filatelefia, PA: Elsevier; 2016: mata 49.

O'Connor OJ, Maher MM. O le urinary tract: aotelega o anatomy, metotia ma radiation mataupu. I totonu: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, eds. Grainger & Allison's Diagnostic Radiology: O Se Tusitusiga o Faʻataʻitaʻiga Faʻataʻitaʻi. 6th ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2015: mata 35.

Shanmugam VK. Vasculitis ma isi mea e le masani ai. I: Sidawy AN, Perler BA, eds. Rutherford's Vascular Surgery ma Endovascular Therapy. 9th ed. Filatelefia, PA: Elsevier; 2019: chap 137

Turnage RH, Mizell J, Badgwell B. puipui o le manava, umbilicus, peritoneum, mesenteries, omentum, ma retroperitoneum. I totonu: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Tusitusiga o Taʻotoga. 20 ed. Filatelefaia, PA: Elsevier Saunders; 2017: mata 43.