Fibrous dysplasia

Fibrous dysplasia o se ponaivi faʻamaʻi e faʻaleagaina ma suia sui masani ponaivi ma fibrous ponaivi ponokalafi. Tasi pe sili atu ponaivi mafai ona afaina.

Fibrous dysplasia masani ona tupu i le taimi o tamaititi. Tele o tagata ua maua faʻailoga ile taimi ua 30 o latou tausaga. O le faʻamaʻi e tupu soo i fafine.

Fibrous dysplasia e fesoʻotaʻi ma se faʻafitauli ma genes (genation mutation) e faʻatonutonu sela-gaosia sela. E tupu le suiga pe a oʻo ina tuputupu aʻe le pepe i le manava. O le tulaga e le pasi mai matua i le tamaititi.

Faʻailoga mafai ono aofia ai soʻo se tasi o mea nei:

• Tiga ponaivi
• O ponaivi (papala)
• Endocrine (homone) faʻafitauli gland
• Fractures poʻo ponaivi faʻaletonu
• Le lanu masani o le paʻu (pigmentation), lea e tupu i le McCune-Albright syndrome

O ponaivi ponaivi mafai ona taofi pe a oʻo i le tamaititi matua.

O le tausi soifua maloloina o le a faia se faʻataʻitaʻiga tino. X-ave o ponaivi ua ave. E ono fautuaina se MRI.

E leai se fofo mo fibrous dysplasia. O ponaivi ponaivi poʻo faʻaletonu e togafitia pe a manaʻomia. E tatau ona togafitia faʻafitauli o ponaivi.

O le vaʻaiga e faʻamoemoe i le ogaoga o le tulaga ma faʻailoga e tupu.

Faʻamoemoeina i ponaivi ua afaina, faʻafitauli tau le soifua maloloina e ono maua mai e aofia ai:

• A afaina le ponaivi ponaivi, e mafai ona iai se vaʻai poʻo se faʻalogo
• A afaina le ponaivi o le vae, ono faigata ona savali ma faʻafesagaʻi faʻafitauli pei o le gugu

Valaʻau lau tautua pe a fai o lau tama o loʻo i ai faʻailoga o lenei tulaga, pei o le toe faia o ponaivi ponaivi ma le le mafaamatalaina ivi ponokalafi.

Faʻapitoa i fomaʻi mata, endocrinology, ma genetics ono aʻafia i le faʻamaoniga ma le tausiga o lau tama.

E leai se auala iloa e puipuia ai fibrous dysplasia. Togafitiga faʻamoemoe e puipuia faʻafitauli, e pei o toe tupu ponaivi ponaivi, e fesoasoani ai i le tulaga faʻaititia laʻititi faigata.

Fula susulu hyperplasia; Idiopathic fibrous hyperplasia; McCune-Albright syndrome

• Anatule auivi i luma

Czerniak B. Fibrous dysplasia ma faʻamaʻi fesoʻotaʻi. I le: Czerniak B, ed. Dorfman ma Czerniak's Bone Tumors. 2nd ed. Filatelefaia, PA: Elsevier Saunders; 2016: mata 8.

Heck RK, Meataalo PC. O ponaivi ponaivi ponaivi ma tulaga nonneoplastic simulate ponaivi ponā. I le: Azar FM, Beaty JH, Canale ST, eds. Campbell's Operative Orthopedics. 13th lomiga. Filatelefia, PA: Elsevier; 2017: mata 25.

Merchant SN, Nadol JB. Faʻaaliga Otologic o faʻamaʻi tino. I le: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Taʻavale ma le ua. 6th ed. Filatelefaia, PA: Elsevier Saunders; 2015: mata 149.

Shiflett JM, Perez AJ, Matua AD. O ulupoʻo i tamaiti: dermoids, langerhans cell histiocytosis, fibrous dysplasia, ma lipomas. I le: Winn HR, ed. Youmans ma Winn Neurological taotoga. 7th ed. Filatelefia, PA: Elsevier; 2017: mata 219