Mucopolysaccharides

Mucopolysaccharides o filifili uumi o suka mumu e maua i le tino atoa, e masani ona i totonu o le mucus ma suamalie faataamilo i soʻoga. E taʻatele na taʻua o glycosaminoglycans.

A le mafai e le tino ona gagau lalo le mucopolysaccharides, e tupu le tulaga e taʻua o le mucopolysaccharidoses (MPS). MPS faʻasino i se kulupu o measina faʻasolosolo o metabolism. Tagata e iai MPS leai ni, pe lava, o se vailaʻau (enzyme) manaʻomia e talepeina i lalo suka filifili mole.

Fomu o MPS aofia ai:

• MPS I (Hurler syndrome; Hurler-Scheie syndrome; Scheie syndrome)
• MPS II (Hunter syndrome)
• MPS III (Sanfilippo syndrome)
• MPS IV (Morquio syndrome)

Glycosaminoglycans; GAG

Kumar V, Abbas AK, Aster JC. Faʻalavelave faʻafitauli I: Kumar V, Abbas AK, Aster JC, eds. Robbins ma Cotran Pathologic Faʻavae o Faamaʻi. 9th ed. Filatelefaia, PA: Elsevier Saunders; 2015: mata 5.

Pyeritz RE. Mauaina faamaʻi o fesoʻotaʻiga aano. I totonu: Goldman L, Schafer AI, eds. Faʻafomaʻi Goldman-Cecil. 26th lomiga. Filatelefia, PA: Elsevier; 2020: mata 244.

Spranger JW. Mucopolysaccharidoses. I le: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Tusitusiga o Pediatrics. 21 ed. Filatelefia, PA: Elsevier; 2020: chap 107.