Tofotofoga Porphyrin

Anotusi

• O a suʻega o le porphyrin?
• O a mea e faʻaaoga ai latou?
• Aisea e manaʻomia ai se suʻega porphyrin?
• Ole a le mea e tupu ile taimi ole faʻataʻitaʻiga ole porphyrin?
• Mata e tatau ona ou faia se mea e sauniuni ai mo le suʻega?
• E i ai ni lamatiaga i le porphyrin suʻega?
• O le a le uiga o faʻaiuga?
• E i ai se isi mea e tatau ona ou iloa e uiga i porphyrin suʻega?
• Faʻamatalaga

O a suʻega o le porphyrin?

O le faʻataʻitaʻiga o le porphyrin e fua ai le maualuga o porphyrins i lou toto, mimi, poʻo le tulaga foʻi. Porphyrins o vailaʻau ia e fesoasoani e fai hemoglobin, o se ituaiga o polotini i ou toto mumu sela. O le hemoglobin e aveina le okesene mai ou mama i vaega o totoe o lou tino.

O se mea masani le i ai o sina laʻititi o porphyrins i lou toto ma isi vai vai. Ae o le tele o le porphyrin atonu o lona uiga oe i ai se ituaiga o porphyria. Porphyria o se le masani ai faʻamaʻi e mafai ona mafua ai matuia faʻafitauli tau soifua maloloina. E masani ona vaevaeina Porphyria i ni vaega se lua:

• Ogaoga porphyrias, lea e masani ona aʻafia ai le neula ma mafua ai faʻailoga o le manava
• Oga mata o porphyrias, lea e mafua ai faʻailoga o le paʻu pe a e faʻaalia i le susulu o le la

Nisi porphyrias aafia uma le neula io ma le paʻu.

Isi igoa: protoporphyrin; protoporphyrin, toto; protoporhyrin, nofoa; porphyrins, otaota; uroporphyrin; porphyrins, miaga; Mauzerall-Granick suʻega; acid; ALA; porphobilinogen; PBG; leai se totogi erythrocyte protoporphyrin; porphyrins erythrocyte vaevaeina; FEP

O a mea e faʻaaoga ai latou?

O faʻataʻitaʻiga ole porphyrin e faʻaaoga e faʻailoaina pe mataʻi ai le porphyria.

Aisea e manaʻomia ai se suʻega porphyrin?

Atonu e te manaʻomia se faʻataʻitaʻiga ole porphyrin peʻa iai sau faʻailoga ole porphyria. E i ai eseʻese faʻailoga mo le eseʻese ituaiga o porphyria.

Faʻailoga o le matuitui porphyria aofia ai:

• Tiga o le manava
• Paneta
• Faanoi ma puaʻi
• Miaga mumu pe enaena
• Maʻi pe lima i lima ma / poʻo vae
• Vaivaiga maso
• Le mautonu
• Faʻaloiga

Faʻailoga o le porphyria faʻaaogaina aofia ai:

• Ova le malamalama i le la
• Mafia i luga o paʻu ua aliali mai i le susulu o le la
• Mūmū ma le fulafula i luga o le paʻu paʻu
• Mageso
• Suiga i le paʻu lanu

Atonu e manaʻomia foʻi se faʻataʻitaʻiga o le porphyrin peʻa iai se tasi o lou aiga e maua i le porphyria. Tele o ituaiga porphyria e maua, o lona uiga o le tulaga pasi mai matua i le tamaititi.

Ole a le mea e tupu ile taimi ole faʻataʻitaʻiga ole porphyrin?

E mafai ona faʻataʻitaʻi le porphyrins ile toto, mimi, poʻo le faʻaui. O loʻo lisi atu i lalo ifo ituaiga o faʻataʻitaʻiga o le porphyrin.

• Tofotofoga Toto
  • O le polofesa mo le soifua maloloina o le a ave se toto faʻataʻitaʻiga mai se uaua i lou lima, faʻaaoga ai se tamaʻi nila. A maeʻa ona tuʻu i totonu le nila, o le a faʻaputuputuina se vaega laʻititi o le toto i totonu o se faʻamaoniga poʻo se ipu. Atonu e te lagonaina sina tiga pe a alu le nila i totonu pe fafo. Lenei masani ona alu ifo i lalo o le lima minute.
• 24-Itula Urine Faʻataʻitaʻiga
  • O le a e aoina uma au miaga i le taimi o le 24-itula vaitaimi. Mo lenei suʻega, o le a avatua e lau tausi soifua maloloina poʻo le fale suʻesuʻe se container ma faʻatonuga faʻapitoa i auala e aoina ai au faʻataʻitaʻiga i le fale. Ia mautinoa e mulimuli ma le faʻaeteete i faʻatonuga uma. Lenei 24-itula urine faʻataʻitaʻiga suʻesuʻega e faʻaaogaina ona o le aofaʻi o vailaʻau i miaga, e aofia ai le porphyrin, mafai ona fesuiaʻi i le aso atoa. Ole faʻaputuputuina la ole tele o faʻataʻitaʻiga ile aso atonu e maua ai se ata sili atu ona saʻo o lau miaga mea.
• Suega o le Urine Random
  • E mafai ona e tuʻuina mai lau faʻataʻitaʻiga i soʻo se taimi o le aso, e aunoa ma ni sauniuniga faʻapitoa poʻo se taulimaina manaʻomia. O lenei suʻega e masani ona faia i le ofisa o le soifua maloloina poʻo le fale suʻesuʻe.
• Tofotofoga Tofotofoga (e taʻua foi o le protoporphyrin i le nofoa)
  • O le ae aoina se faʻataʻitaʻiga o lau nofoa ma tuʻu i totonu o se fagu faʻapitoa. O lau fomaʻi tausi soifua o le a avatua ia te oe faʻatonuga i le auala e saunia ai lau faʻataʻitaʻiga ma lafo atu i se fale suesue.

Mata e tatau ona ou faia se mea e sauniuni ai mo le suʻega?

E te le manaʻomia ni sauniuniga faʻapitoa mo suʻega ole toto poʻo le urine.

Mo se faʻataʻitaʻiga nofoaʻiga, oe ono faatonuina oe e aua le 'aʻai aano o manu pe ave ni vailaʻau o loʻo i ai aspirin mo le tolu aso ae le i faia lau suʻega.

E i ai ni lamatiaga i le porphyrin suʻega?

E laʻititi lava le aʻafia ile faia ole suʻega ile toto. E i ai sina tiga poʻo se tiga i le mea na tuu ai le nila, ae o le tele o faʻailoga e vave ona alu ese.

E i ai le iloa lamatiaga i miaga poʻo faʻataʻitaʻiga suʻega.

O le a le uiga o faʻaiuga?

Afai e maua le maualuga o le porphyrin i lou toto, miaga, poʻo le nofoa, atonu o le a okaina e lau tausi soifua maloloina nisi suʻesuʻega e faʻamaonia ai se faʻamaoniga ma ia iloa ai le ituaiga o porphyria o loʻo ia oe. A o leai se fofo mo porphyria, o le tulaga mafai ona pulea. Nisi suiga olaga ma / poʻo vailaʻau mafai ona fesoasoani puipuia faʻailoga ma faʻafitauli o le faʻamaʻi. O togafitiga faʻapitoa e faʻamoemoeina i le ituaiga o porphyria o loʻo ia te oe. A iai ni au fesili e uiga i au iʻuga pe e uiga i le porphyria, talanoa i lau fomaʻi.

Aʻoaʻo atili e uiga i suʻesuʻega falesuesue, vaitau o faʻasino, ma malamalamaaga i iʻuga

E i ai se isi mea e tatau ona ou iloa e uiga i porphyrin suʻega?

E ui o le tele o ituaiga o porphyria e maua, o isi ituaiga porphyria e mafai foi ona maua. O le mauaina o le porphyria e mafai ona mafua mai i ni mea eseese, e aofia ai le soona faailoa atu i le taʻitaʻi, HIV, hepatitis C, soona inu uʻamea, ma / poʻo le soʻona inu 'ava malosi.

Faʻamatalaga

1. American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. E uiga ia Porphyria; [taua i le 2019 Tes 26]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria
2. American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. Porphyrins ma Porphyria Diagnosis; [taua i le 2019 Tes 26]; [pe a ma le 6 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
3. American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. Laina Muamua Suʻega; [taua i le 2019 Tes 26]; [tusa o le 4 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
4. Hepatitis B Foundation [Initaneti]. Doylestown (PA): Hepb.org; c2017. Masani Metabolic Faamaʻi; [sii mai 2017 Tesema 20]; [pe a ma le 11 pupuni] Avanoa mai: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
5. Hinkle J, Cheever K. Brunner & Suddarth's Handbook of Laboratory and Diagnostic Tests. 2nd Ed, faamumū. Filatelefaia: Wolters Kluwer Soifua Maloloina, Lippincott Williams & Wilkins; c2014. Fractionated Erythrocyte Porphyrins (FEP); i. 308.
6. Lab Tofotofoga lugalaina [Initaneti]. American Association mo vailaʻau Togafitiga; c2001–2017. Lomifefiloi: Random Urine Sample; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni]Avanoa mai: https://labtestsonline.org/glossary#r
7. Lab Tofotofoga lugalaina [Initaneti]. American Association mo vailaʻau Togafitiga; c2001–2017. Faʻataʻitaʻiga o le Porphyrin; [faafou 2017 Tes 20; taʻua 2017 Dec 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://labtestsonline.org/tests/porphyrin-tests
8. Mayo Clinic [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1998–2017. Porphyria: Faʻailoga ma Mafuaʻaga; 2017 Nov 18 [taʻua 2017 Dec 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
9. Mayo Clinic: Mayo Medical Laboratories [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1995–2017. ID faʻataʻitaʻi: FQPPS: Porphyrins, Feces: Vaaiga lautele; [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
10. Mayo Clinic: Mayo Medical Laboratories [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1995–2017. ID faʻataʻitaʻi: FQPPS: Porphyrins, Feces: Faʻataʻitaʻiga; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
11. Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Matuʻi Faʻasolosolo Porphyria; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/acute-intermittent-porphyria
12. Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Vaaiga aoao o Porphyria; [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/overview-of-porphyria
13. Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Porphyria Cutanea Tarda; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/porphyria-cutanea-tarda
14. National Heart, Lung, and Blood Institute [Initaneti]. Bethesda (MD): U.S. Matagaluega o le Soifua Maloloina ma Tagata Auaunaga; Tofotofoga Toto; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.nhlbi.nih.gov/health-topics/blood-tests
15. National Institute of Diabetes ma Digestive ma Fatugaʻo Faamaʻi [Initaneti]. Bethesda (MD): U.S. Matagaluega o le Soifua Maloloina ma Tagata Auaunaga; Porphyria; 2014 Fepuari [taʻua 2017 Tesema 20]; [tusa o le 4 pupuni] Avanoa mai: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
16. Iunivesite o Rochester Medical Center [Initaneti]. Rochester (NY): Iunivesite o Rochester Medical Center; c2017. Health Encyclopedia: Porphyrins (Urine); [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine

O faʻamatalaga i luga o lenei 'upega tafaʻilagi e le tatau ona faʻaaogaina e fai ma sui o fomaʻi faʻapitoa togafitiga poʻo fautuaga. Faʻafesoʻotaʻi le au tausi soifua pe a iai ni au fesili e uiga i lou soifua maloloina.