Tofotofoga Porphyrin
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Anotusi
- O a suʻega o le porphyrin?
- O a mea e faʻaaoga ai latou?
- Aisea e manaʻomia ai se suʻega porphyrin?
- Ole a le mea e tupu ile taimi ole faʻataʻitaʻiga ole porphyrin?
- Mata e tatau ona ou faia se mea e sauniuni ai mo le suʻega?
- E i ai ni lamatiaga i le porphyrin suʻega?
- O le a le uiga o faʻaiuga?
- E i ai se isi mea e tatau ona ou iloa e uiga i porphyrin suʻega?
- Faʻamatalaga
O a suʻega o le porphyrin?
O le faʻataʻitaʻiga o le porphyrin e fua ai le maualuga o porphyrins i lou toto, mimi, poʻo le tulaga foʻi. Porphyrins o vailaʻau ia e fesoasoani e fai hemoglobin, o se ituaiga o polotini i ou toto mumu sela. O le hemoglobin e aveina le okesene mai ou mama i vaega o totoe o lou tino.
O se mea masani le i ai o sina laʻititi o porphyrins i lou toto ma isi vai vai. Ae o le tele o le porphyrin atonu o lona uiga oe i ai se ituaiga o porphyria. Porphyria o se le masani ai faʻamaʻi e mafai ona mafua ai matuia faʻafitauli tau soifua maloloina. E masani ona vaevaeina Porphyria i ni vaega se lua:
- Ogaoga porphyrias, lea e masani ona aʻafia ai le neula ma mafua ai faʻailoga o le manava
- Oga mata o porphyrias, lea e mafua ai faʻailoga o le paʻu pe a e faʻaalia i le susulu o le la
Nisi porphyrias aafia uma le neula io ma le paʻu.
Isi igoa: protoporphyrin; protoporphyrin, toto; protoporhyrin, nofoa; porphyrins, otaota; uroporphyrin; porphyrins, miaga; Mauzerall-Granick suʻega; acid; ALA; porphobilinogen; PBG; leai se totogi erythrocyte protoporphyrin; porphyrins erythrocyte vaevaeina; FEP
O a mea e faʻaaoga ai latou?
O faʻataʻitaʻiga ole porphyrin e faʻaaoga e faʻailoaina pe mataʻi ai le porphyria.
Aisea e manaʻomia ai se suʻega porphyrin?
Atonu e te manaʻomia se faʻataʻitaʻiga ole porphyrin peʻa iai sau faʻailoga ole porphyria. E i ai eseʻese faʻailoga mo le eseʻese ituaiga o porphyria.
Faʻailoga o le matuitui porphyria aofia ai:
- Tiga o le manava
- Paneta
- Faanoi ma puaʻi
- Miaga mumu pe enaena
- Maʻi pe lima i lima ma / poʻo vae
- Vaivaiga maso
- Le mautonu
- Faʻaloiga
Faʻailoga o le porphyria faʻaaogaina aofia ai:
- Ova le malamalama i le la
- Mafia i luga o paʻu ua aliali mai i le susulu o le la
- Mūmū ma le fulafula i luga o le paʻu paʻu
- Mageso
- Suiga i le paʻu lanu
Atonu e manaʻomia foʻi se faʻataʻitaʻiga o le porphyrin peʻa iai se tasi o lou aiga e maua i le porphyria. Tele o ituaiga porphyria e maua, o lona uiga o le tulaga pasi mai matua i le tamaititi.
Ole a le mea e tupu ile taimi ole faʻataʻitaʻiga ole porphyrin?
E mafai ona faʻataʻitaʻi le porphyrins ile toto, mimi, poʻo le faʻaui. O loʻo lisi atu i lalo ifo ituaiga o faʻataʻitaʻiga o le porphyrin.
- Tofotofoga Toto
- O le polofesa mo le soifua maloloina o le a ave se toto faʻataʻitaʻiga mai se uaua i lou lima, faʻaaoga ai se tamaʻi nila. A maeʻa ona tuʻu i totonu le nila, o le a faʻaputuputuina se vaega laʻititi o le toto i totonu o se faʻamaoniga poʻo se ipu. Atonu e te lagonaina sina tiga pe a alu le nila i totonu pe fafo. Lenei masani ona alu ifo i lalo o le lima minute.
- 24-Itula Urine Faʻataʻitaʻiga
- O le a e aoina uma au miaga i le taimi o le 24-itula vaitaimi. Mo lenei suʻega, o le a avatua e lau tausi soifua maloloina poʻo le fale suʻesuʻe se container ma faʻatonuga faʻapitoa i auala e aoina ai au faʻataʻitaʻiga i le fale. Ia mautinoa e mulimuli ma le faʻaeteete i faʻatonuga uma. Lenei 24-itula urine faʻataʻitaʻiga suʻesuʻega e faʻaaogaina ona o le aofaʻi o vailaʻau i miaga, e aofia ai le porphyrin, mafai ona fesuiaʻi i le aso atoa. Ole faʻaputuputuina la ole tele o faʻataʻitaʻiga ile aso atonu e maua ai se ata sili atu ona saʻo o lau miaga mea.
- Suega o le Urine Random
- E mafai ona e tuʻuina mai lau faʻataʻitaʻiga i soʻo se taimi o le aso, e aunoa ma ni sauniuniga faʻapitoa poʻo se taulimaina manaʻomia. O lenei suʻega e masani ona faia i le ofisa o le soifua maloloina poʻo le fale suʻesuʻe.
- Tofotofoga Tofotofoga (e taʻua foi o le protoporphyrin i le nofoa)
- O le ae aoina se faʻataʻitaʻiga o lau nofoa ma tuʻu i totonu o se fagu faʻapitoa. O lau fomaʻi tausi soifua o le a avatua ia te oe faʻatonuga i le auala e saunia ai lau faʻataʻitaʻiga ma lafo atu i se fale suesue.
Mata e tatau ona ou faia se mea e sauniuni ai mo le suʻega?
E te le manaʻomia ni sauniuniga faʻapitoa mo suʻega ole toto poʻo le urine.
Mo se faʻataʻitaʻiga nofoaʻiga, oe ono faatonuina oe e aua le 'aʻai aano o manu pe ave ni vailaʻau o loʻo i ai aspirin mo le tolu aso ae le i faia lau suʻega.
E i ai ni lamatiaga i le porphyrin suʻega?
E laʻititi lava le aʻafia ile faia ole suʻega ile toto. E i ai sina tiga poʻo se tiga i le mea na tuu ai le nila, ae o le tele o faʻailoga e vave ona alu ese.
E i ai le iloa lamatiaga i miaga poʻo faʻataʻitaʻiga suʻega.
O le a le uiga o faʻaiuga?
Afai e maua le maualuga o le porphyrin i lou toto, miaga, poʻo le nofoa, atonu o le a okaina e lau tausi soifua maloloina nisi suʻesuʻega e faʻamaonia ai se faʻamaoniga ma ia iloa ai le ituaiga o porphyria o loʻo ia oe. A o leai se fofo mo porphyria, o le tulaga mafai ona pulea. Nisi suiga olaga ma / poʻo vailaʻau mafai ona fesoasoani puipuia faʻailoga ma faʻafitauli o le faʻamaʻi. O togafitiga faʻapitoa e faʻamoemoeina i le ituaiga o porphyria o loʻo ia te oe. A iai ni au fesili e uiga i au iʻuga pe e uiga i le porphyria, talanoa i lau fomaʻi.
Aʻoaʻo atili e uiga i suʻesuʻega falesuesue, vaitau o faʻasino, ma malamalamaaga i iʻuga
E i ai se isi mea e tatau ona ou iloa e uiga i porphyrin suʻega?
E ui o le tele o ituaiga o porphyria e maua, o isi ituaiga porphyria e mafai foi ona maua. O le mauaina o le porphyria e mafai ona mafua mai i ni mea eseese, e aofia ai le soona faailoa atu i le taʻitaʻi, HIV, hepatitis C, soona inu uʻamea, ma / poʻo le soʻona inu 'ava malosi.
Faʻamatalaga
- American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. E uiga ia Porphyria; [taua i le 2019 Tes 26]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria
- American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. Porphyrins ma Porphyria Diagnosis; [taua i le 2019 Tes 26]; [pe a ma le 6 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
- American Porphyria Foundation [Initaneti]. Houston: American Porphyria Foundation; c2010–2017. Laina Muamua Suʻega; [taua i le 2019 Tes 26]; [tusa o le 4 pupuni] Avanoa mai: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
- Hepatitis B Foundation [Initaneti]. Doylestown (PA): Hepb.org; c2017. Masani Metabolic Faamaʻi; [sii mai 2017 Tesema 20]; [pe a ma le 11 pupuni] Avanoa mai: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
- Hinkle J, Cheever K. Brunner & Suddarth's Handbook of Laboratory and Diagnostic Tests. 2nd Ed, faamumū. Filatelefaia: Wolters Kluwer Soifua Maloloina, Lippincott Williams & Wilkins; c2014. Fractionated Erythrocyte Porphyrins (FEP); i. 308.
- Lab Tofotofoga lugalaina [Initaneti]. American Association mo vailaʻau Togafitiga; c2001–2017. Lomifefiloi: Random Urine Sample; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni]Avanoa mai: https://labtestsonline.org/glossary#r
- Lab Tofotofoga lugalaina [Initaneti]. American Association mo vailaʻau Togafitiga; c2001–2017. Faʻataʻitaʻiga o le Porphyrin; [faafou 2017 Tes 20; taʻua 2017 Dec 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://labtestsonline.org/tests/porphyrin-tests
- Mayo Clinic [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1998–2017. Porphyria: Faʻailoga ma Mafuaʻaga; 2017 Nov 18 [taʻua 2017 Dec 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
- Mayo Clinic: Mayo Medical Laboratories [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1995–2017. ID faʻataʻitaʻi: FQPPS: Porphyrins, Feces: Vaaiga lautele; [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
- Mayo Clinic: Mayo Medical Laboratories [Initaneti]. Mayo Faʻavae mo Aʻoga Faʻafomaʻi ma Suesuega; c1995–2017. ID faʻataʻitaʻi: FQPPS: Porphyrins, Feces: Faʻataʻitaʻiga; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
- Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Matuʻi Faʻasolosolo Porphyria; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/acute-intermittent-porphyria
- Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Vaaiga aoao o Porphyria; [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/overview-of-porphyria
- Merck Manual Consumer Version [Initaneti]. Kenilworth (NJ): Merck & Co. Inc. c2017. Porphyria Cutanea Tarda; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/porphyria-cutanea-tarda
- National Heart, Lung, and Blood Institute [Initaneti]. Bethesda (MD): U.S. Matagaluega o le Soifua Maloloina ma Tagata Auaunaga; Tofotofoga Toto; [sii mai 2017 Tesema 20]; [pe tusa ma le 3 pupuni] Avanoa mai: https://www.nhlbi.nih.gov/health-topics/blood-tests
- National Institute of Diabetes ma Digestive ma Fatugaʻo Faamaʻi [Initaneti]. Bethesda (MD): U.S. Matagaluega o le Soifua Maloloina ma Tagata Auaunaga; Porphyria; 2014 Fepuari [taʻua 2017 Tesema 20]; [tusa o le 4 pupuni] Avanoa mai: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
- Iunivesite o Rochester Medical Center [Initaneti]. Rochester (NY): Iunivesite o Rochester Medical Center; c2017. Health Encyclopedia: Porphyrins (Urine); [sii mai 2017 Tesema 20]; [pe a ma le 2 pupuni] Avanoa mai: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine
O faʻamatalaga i luga o lenei 'upega tafaʻilagi e le tatau ona faʻaaogaina e fai ma sui o fomaʻi faʻapitoa togafitiga poʻo fautuaga. Faʻafesoʻotaʻi le au tausi soifua pe a iai ni au fesili e uiga i lou soifua maloloina.