Fibrosis pulmonary Idiopathic

Idiopathic pulmonary fibrosis (IPF) o maʻila pe mafiafia o mama e aunoa ma se mafuaʻaga iloa.

E le iloa e tausi soifua maloloina mea e mafua ai le IPF pe aisea e atia ai e nisi tagata. Idiopathic o lona uiga e leʻo iloa le mafuaʻaga. O le tulaga ono mafua mai i le mama tali atu i se le iloa vailaʻau poʻo manuʻa. E ono faʻatinoina e Genes se sao i le atiaʻe o le IPF. O le faʻamaʻi e tupu soo i tagata i le va o le 60 ma le 70 tausaga. IPF e sili ona taatele i alii nai lo fafine.

A i ai sau IPF, o ou mama e maʻila ma malo. Ua faigata ai ia te oe ona manava. I le tele o tagata, o le IPF e atili ai ona leaga i le tele o masina poʻo ni nai tausaga. I isi, o le IPF e atili ai ona leaga i se taimi umi.

Faʻailoga mafai ono aofia ai soʻo se tasi o mea nei:

• Tiga o le fatafata (o isi taimi)
• Mama (masani lava ona mago)
• Le mafai ona toe toaga mai pei o le taimi muamua
• Paʻu le manava i le taimi o gaioiga (o lenei faʻailoga tumau mo masina po o tausaga, ma i le aluga o taimi ono tupu foi pe a malolo)
• Lagona ua matapogia
• Faasolosolo lemu pauna

Ole suʻega o le a faia se suʻega faʻaletino ma fesili e uiga i lau talaʻiga faʻafomaʻi. O le a fesiligia oe pe na e aafia i asbestos poʻo isi vailaʻau oona ma pe a fai o oe o se tagata ulaula.

O le suʻega faʻaletino atonu e te maua ai:

• Ole manava masani e taʻua ole paʻu
• Paʻu lanumoana (cyanosis) faʻataʻamilo i le gutu poʻo atigilima ona o le maualalo o le okesene (ma faʻamaʻi maualuluga)
• Faʻateleina ma le faʻapipiʻiina o tamaʻilima vae, e taʻua o le kalapu (ma le faʻamaʻi oʻo atu)

Suʻega e fesoasoani faʻailoaina IPF aofia ai mea nei:

• Bronchoscopy
• Maualuga maualuga CT scan scan (HRCT)
• Fatafata x-ray
• Echocardiogram
• Fua o le toto maualuga maualuga okesene (arterial toto kasa)
• Suʻesuʻega o le pulmonary function
• 6-minute savali suʻega
• Suʻega mo faʻamaʻi autoimmune pei o rheumatoid gugu, lupus, poʻo le scleroderma
• Tatala māmā (taotoga) māmā biopsy

E leai se faʻailoaina lauiloa mo IPF.

Togafitiga e faʻatatau i le faʻamamaina o faʻailoga ma telegese faʻamaʻi alualu i luma:

• Pirfenidone (Esbriet) ma nintedanib (Ofev) o vailaʻau e lua e togafitia ai le IPF. Atonu latou te fesoasoani e faʻatelegese le faʻaleagaina o māmā
• Tagata e maualalo le maualuga o le okesene o le a manaʻomia le okesene lagolago i le fale.
• E le mafai ona faʻamalolo le maʻi ile toe faʻaleleia o le mama, ae mafai ona fesoasoani i tagata e faʻamalositino ma laʻititi ifo le manava.

Faia o le fale ma olaga sitaili suiga mafai ona fesoasoani faʻatonutonu manava faʻailoga. Afai o oe poʻo ni tagata o le aiga e ulaula, o le taimi lenei e taofi ai.

E mafai ona iloiloina se toto mo nisi tagata e iai le IPF alualu i luma.

Oe mafai ona faʻafaigofieina le popolevale o maʻi i le auai i se vaega lagolago. O le fefaʻasoaaʻi ma isi e masani ona maua ni faʻafitauli ma faʻafitauli e mafai ona fesoasoani ia te oe e te le lagona ai le tuua toʻatasi.

Nisi faʻamatalaga ma fesoasoani mo tagata e iai le IPF ma o latou aiga e mafai ona maua i:

• Pulmonary Fibrosis Foundation - www.pulmonaryfibrosis.org/life-with-pf/support-groups
• American Lung Association - www.lung.org/support-and-community/

IPF ono faʻaleleia pe tumau tumau mo se taimi umi ma pe leai ni togafitiga. Tele o tagata ua atili ai ona leaga, e oʻo lava i togafitiga.

A oʻo ina tigaina auga manava, o oe ma lau tautua e tatau ona talanoaina togafitiga e faʻafualoa ai le ola, pei o le aveina o mama. Faʻatalanoa foʻi muamua le fuafuaina o tausiga.

Faʻafitauli o le IPF ono aofia ai:

• Maualuga maualuga o sela mumu toto ona o le maualalo le toto maualuga oxygen
• Pulu malepe
• Toto maualuga i alatoto o mama
• Faʻamalologa manava
• Cor pulmonale (itu taumatau fatu fatu)
• Oti

Valaau vave lau tautua peʻa iai sau mea nei:

• Manava e sili atu le faigata, saoasaoa pe papaʻu (oe le mafai ona manava loloa)
• Ia faalagolago i luma pe a nofo e manava lelei
• Tele ulu tiga
• Moe po o le le mautonu
• Fiva
• Sole pouliuli pe a e tale
• Lanumoana limamata lima poʻo le paʻu i ou atigilima

Idiopathic faataapeapeina interstitial pulmonary fibrosis; IPF; Falaʻau pulmonary; Cryptogenic fibrosing alveolitis; CFA; Fibrosing alveolitis; Masani interstitial pneumonitis; UIP

• Faʻaaogaina okesene i le fale

• Spirometry
• Kalapu
• Respiratory system

National Heart, Lung, ma le Blood Institute 'upega tafaʻilagi. Fibrosis pulmonary Idiopathic. www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. Avanoa Ianuari 13, 2020.

Raghu G, Martinez FJ. Faʻamaʻi pipisi i totonu ole mama. I totonu: Goldman L, Schafer AI, eds. Faʻafomaʻi Goldman-Cecil. 26th lomiga. Filatelefia, PA: Elsevier; 2020: chap 86.

Raghu G, Rochwerg B, Zhang Y, et al. O se ATS / ERS / JRS / ALAT faʻataʻitaʻi faʻataʻitaʻi falemaʻi faʻapitoa: togafitiga o le idiopathic pulmonary fibrosis. O se faʻafouga o le 2011 togafitiga faʻataʻiala taʻiala. Am J Respir Crit Care Med. 2015; 192 (2): e3-e19. PMID: 26177183 pubmed.ncbi.nlm.nih.gov/26177183/.

Ryu JH, Selman M, Colby TV, King TE. Idiopathic interstitial pneumonias. I: Broaddus VC, Mason RJ, Ernst JD, et al, eds. Murray ma Nadel's Textbook of Respiratory Medicine. 6th ed. Filatelefaia, PA: Elsevier Saunders; 2016: mata 63.

Silhan LL, Danoff SK. Nonpharmacologic togafitiga mo idiopathic pulmonary fibrosis. I: Collard HR, Richeldi L, eds. Faamaʻi pipisi i totonu ole va. Filatelefia, PA: Elsevier; 2018: mata 5.