Pulmonary veno-occlusive faʻamaʻi

Pulmonary veno-occlusive faamaʻi (PVOD) o se faamaʻi seasea lava. E tau atu i le toto maualuga i alatoto o le mama (pulmonary hypertension).

I le tele o tulaga, o le mafuaʻaga o le PVOD e leʻo iloaina. Ole toto maualuga e tupu ile alatoto ole alatoto. O nei alatoto mama e fesoʻotaʻi saʻo i le itu taumatau o le fatu.

O le tulaga e ono fesoʻotaʻi ma se faʻamaʻi viral. E mafai ona tupu o se faʻalavelave o nisi faʻamaʻi pei o le lupus, poʻo le gaʻo o le ponaivi.

O le faʻamaʻi e sili ona taatele i tamaiti ma talavou matutua. A o atili ai le faʻamaʻi, e mafua ai:

• Vaʻaigai alatoto
• Toto toto maualuga
• Faʻalavelave ma fulafula o mama

Faʻafitauli e ono lamatia ai mo le PVOD aofia ai:

• Talafaʻasolopito o aiga o le tulaga
• Ulaula
• Faʻaalia i vailaʻau pei o trichlorethylene poʻo chemotherapy vailaʻau
• Systemic sclerosis (autoimmune paʻu faʻaletonu)

Faʻailoga mafai ono aofia ai soʻo se tasi o mea nei:

• Manava le mānava
• Tale mama
• Le lava ile faʻamalosi tino
• Fainting
• Mauaina le toto
• Faigata le manava a o taatia laugatasi

O le a suʻesuʻe oe e le tausi soifua maloloina ma fesili e uiga i lau soifua maloloina talaʻaga ma faʻailoga.

E ono faʻaalia i le suʻega:

• Faʻateleina le mamafa i ua o le ua
• Faʻapipiʻiina o tamailima
• Lanumoana lanu o le paʻu ona o le leai o le okesene (cyanosis)
• Fula i vae

Atonu e lagona e lau tautua le le masani o le fatu pe a faʻalogo i le fatafata ma mama ma le stethoscope.

O suʻega ia e ono faia:

• Kesi toto Arterial
• Toto oximetry
• Fatafata x-ray
• Fatafata CT
• Catheterization fatu
• Luga gaioiga suʻega
• Echocardiogram
• Biopsy o le mama

E leʻo i ai nei se lauiloa togafitiga faʻafomaʻi aoga. Ae ui i lea, o vailaʻau nei e ono aoga mo nisi tagata:

• Vailaau e faʻalauteleina le alatoto (vasodilators)
• Vailaau e faʻatonutonu le tali atu o le puipuiga (pei o azathioprine poʻo vailaʻau)

E manaʻomia se taulaʻi mama.

O le iʻuga e masani ona matua matitiva lava i pepe, ma le saoasaoa o fua faatatau na o ni nai vaiaso. Ola i tagata matutua ono masina i ni nai tausaga.

Faʻafitauli o le PVOD ono aofia ai:

• Faigata manava e sili atu ona leaga, aofia ai i le po (moe apnea)
• Toto maualuga
• Lelei itu fatu taumatau (cor pulmonale)

Valaʻau lau tautua pe a fai oe maua faʻailoga o lenei faʻamaʻi.

Maʻi vaso-faʻapitoa faʻamaʻi

• Respiratory system

Chin K, Channick RN. Toto maualuga I: Broaddus VC, Mason RJ, Ernst JD, et al, eds. Murray ma Nadel's Textbook of Respiratory Medicine. 6th ed.Filatelefaia, PA: Elsevier Saunders; 2016: mata 58.

Churg A, Wright JL. Toto maualuga I: Leslie KO, Wick MR, eds. Faʻataʻitaʻiga Pulmonary Pathology: O Se Suʻega Suʻesuʻe. 3rd ed. Filatelefia, PA: Elsevier; 2018: mata 12.

Mclaughlin VV, Humbert M. Pulmonary toto maualuga I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald's Heart Disease: O Se Tusitusiga o Faʻafomaʻi Cardiovascular. 11th lomiga. Filatelefia, PA: Elsevier; 2019: chap 85.