Aiga lipoprotein lipase le atoatoa

Aiga lipoprotein lipase le lava o se vaega o le seasea tupuʻaga faʻamaʻi lea e le maua ai e se tagata se polotini manaʻomia e talepe i lalo gaʻo mole. O le faʻamaʻi mafua ai le tele o gaʻo e faaputuputu i le toto.

Aiga iloga lipoprotein lipase le atoatoa e mafua mai i se le atoatoa gafa ua pasia i lalo e ala i aiga.

O tagata e maua i lenei tulaga e leai se enzyme e taʻua o le lipoprotein lipase. A aunoa ma lenei enzyme, e le mafai e le tino ona gagauina le gaʻo mai meaʻai ua faʻaleagaina. O gaʻo gaʻo e taʻua o le chylomicrons e tupu aʻe i le toto.

Tulaga lamatia aofia ai se aiga talaʻaga o lipoprotein lipase le atoatoa.

O le tulaga e masani ona muamua vaʻaia i le taimi o pepe pe tamaititi.

Faʻailoga mafai ono aofia ai soʻo se tasi o mea nei:

• Manava o le manava (atonu e foliga mai o colic i pepe)
• Leai o le fiaai
• Faanoi, puaʻi
• Tiga i maso ma ponaivi
• Faalauteleina ate ma spleen
• Le mafai ona olaola i pepe
• Puta gaʻo i le paʻu (xanthomas)
• Maualuga triglyceride tulaga i le toto
• Paʻu retina ma papaʻe lanu paʻepaʻe toto i le retina
• Fiva mumu o le pancreas
• Lanu samasama o mata ma le paʻu (jaundice)

O le tausi soifua maloloina o le a faia se faʻataʻitaʻiga tino ma fesili e uiga i faʻailoga.

Toto suʻega o le a faia e siaki ai le toto ma triglyceride tulaga. O isi taimi, o se faʻapitoa suʻesuʻe toto e faia pe a maeʻa ona tuʻuina ia oe manifinifi toto ala i se alatoto. Lenei suʻega vaʻai mo lipoprotein lipase gaioiga i lou toto.

E mafai ona faia suʻega o kenera.

Togafitiga faʻamoemoe e faʻatonutonu ia faʻailoga ma le toto triglyceride maualuga ma se meaʻai maualalo tele-gaʻo. E ono fautuaina oe e lau tautua oe aua neʻi sili atu i le 20 kalama gaʻo i le aso e taofia ai le toe foʻi mai o faʻailoga.

Luasefulu kalama o gaʻo e tutusa ma se tasi o mea nei:

• Lua 8-aunese (240 mililita) ipu malamalama o le susu atoa
• 4 sipuni sipuni (9.5 kalama) o margarine
• 4 aunese (113 kalama) tautua aano o aano o manufasi

Ole averesi o taumafataga a Amerika e iai le lololo o mea e oʻo ile 45% ole aofaʻi o kalori. O fualaʻau e mafai ona faʻaalu ile gaʻo, A, D, E, ma le K ma minerale faʻaopopo e fautuaina mo tagata e 'aʻai i se taumafataga paʻu maualalo. Atonu e te manaʻo e talanoaina au meaʻai manaʻomia ma lau tausimaʻi ma lau lesitalaina o meaʻai.

Pancreatitis e fesoʻotaʻi ma le le lava o le lipoprotein lipase tali atu i togafitiga mo lena maʻi.

O nei punaʻoa mafai ona maua ai nisi faʻamatalaga e uiga i aiga lipoprotein lipase le atoatoa:

• National Organization for Rare Disorder - rarediseases.org/rare-diseases/familial-lipoprotein-lipase-deficiency
• NIH Genetics Fale Faʻasino Tusi - ghr.nlm.nih.gov/condition/familial-lipoprotein-lipase-deficiency

O tagata e iai le faʻamaʻi lea e mulimuli i le taumafataga paʻu maualalo e mafai ona avea ma tagata matua.

Pancreatitis ma toe tupu vaega o tiga manava ono tupu.

Xanthomas e le masani ona tiga seʻi vagana ua latou olo tele.

Valaʻau lau tautua mo le suʻesuʻeina pe a fai o se tasi o lou aiga e le atoatoa le lipoprotein lipase. O fautuaga faʻapitoa e fautuaina mo soʻo se tasi e iai se talaʻaga a le aiga o lenei faʻamaʻi.

E leai se iloa puipuia mo lenei le masani ai, tofi tuufaasolo. Faʻalauiloaina o lamatiaga ono faʻatagaina vave maua. I le maeʻa ai o se meaʻai maualalo le gaʻoa mafai ona faʻaleleia atili ai faʻailoga o lenei faʻamaʻi.

Ituaiga I hyperlipoproteinemia; Aiga chylomicronemia; Le lava aiga LPL

• Faʻamaʻi o alatoto toto

Genest J, Libby P. Lipoprotein faʻafitauli ma faʻamaʻi fatu. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald's Heart Disease: O Se Tusitusiga o Faʻafomaʻi Cardiovascular. 11th lomiga. Filatelefia, PA: Elsevier; 2019: chap 48.

Semenkovich CF, Goldberg AC, Goldberg IJ. Faʻaletonu o le lipid metabolism. I: Melmed S, Polonsky KS, Larsen PR, Kronenberg HM, eds. Williams Tusitusiga o Endocrinology. 13th lomiga. Filatelefia, PA: Elsevier; 2016: mata 37.