Eosinophilic fasciitis

O le Eosinophilic fasciitis (EF) o se faʻamaʻi o le tino lea e i lalo o le paʻu ma luga o maso, e taʻua o le fascia, e fulafula, mumu ma mafiafia. O le paʻu i lima, vae, ua, manava poʻo vae e mafai ona fulafula vave. E seasea tupu le tulaga.

EF foliga foliga tutusa ma scleroderma, ae le fesoʻotaʻi. E le pei ole scleroderma, ile EF, e leʻo aʻafia ai tamailima.

O le mafuaʻaga o le EF e leʻo iloa. E seasea lava ni mataupu na tutupu ina ua maeʻa ona ave le L-tryptophan supplement. I tagata e iai lenei faʻamaʻi, o sela papaʻe e taʻua o eosinofil, e tutupu aʻe i maso ma maso. Eosinophils e fesoʻotaʻi ma tali atu i faʻamaʻi. O le faʻamaʻi e sili ona taatele i tagata mai le 30 i le 60 tausaga.

Faʻailoga e ono aofia ai:

• Malu ma fulafula o le paʻu i lima, vae, poʻo nisi taimi soʻoga (o le tele o taimi i itu uma o le tino)
• Gugu
• Carpal auala faʻafafa
• Tiga maso
• Paʻu mafiafia e foliga faʻaputu

O suʻega e mafai ona faia e aofia ai:

• CBC ma eseesega
• Gamma globulins (o se ituaiga o puipuiga faʻafitauli protein)
• Fua faatatau sedryation Erythrocyte (ESR)
• MRI
• Maso biopsy
• Paʻu biopsy (le biopsy manaʻomia e aofia ai le loloto aano o le fascia)

Corticosteroids ma isi vailaʻau puipuia-taofiofia vailaʻau e faʻaaogaina e faʻamama ai auga. O nei vailaʻau e sili atu le aoga pe a amata vave i le faʻamaʻi. O fualaʻau e le faʻaaoga e puipuia ai le mafaufau (NSAIDs) e mafai foi ona fesoasoani e faʻaititia ai faʻailoga.

I le tele o tulaga, o le tulaga alu ese i totonu o le 1 i le 3 tausaga. Peitaʻi, o faʻailoga e ono umi atu pe toe foʻi mai.

O le gugu o se faʻalavelave e seasea tupu i le EF. O nisi tagata e ono aʻafia i faʻamaʻi toto tele poʻo kanesa e faʻatatau i le toto, pei o le aplastic anemia poʻo leukemia. O le vaaiga e sili atu ona leaga pe a fai o faʻamaʻi toto.

Valaʻau lau fomaʻi pe a fai o loʻo e maua i faʻamaʻi o lenei faʻamaʻi.

E leai se iloa puipuia.

Shulman syndrome

• Musele pito i luma o maso

Aronson JK. Tapetopa. I le: Aronson JK, ed. Meyler's Side Effects o Fualaʻau. 16th lomiga. Waltham, MA: Elsevier B.V.; 2016: 220-221.

James WD, Elston DM, Togafitiga JR, Rosenbach MA, Neuhaus IM. Faamai fesoʻotaʻiga. I totonu: James WD, Elston DM, Treat JR, Rosenbach MA, Neuhaus IM, eds. Andrews 'Faamaʻi o le Paʻu: Clinical Dermatology. 13th lomiga. Filatelefia, PA: Elsevier; 2020: mata 8.

Lee LA, Werth VP. Paʻu ma faʻamaʻi rumatika. I totonu: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Kelley ma Firestein's Tusitusiga o Rheumatology. 10 ed. Filatelefia, PA: Elsevier; 2017: mata 43.

Pinal-Fernandez I, Selva-O ’Callaghan A, Grau JM. Faʻailoaina ma faʻavasegaina o eosinophilic fasciitis. Autoimmun Rev.. 2014; 13 (4-5): 379-382. PMID: 24424187 www.ncbi.nlm.nih.gov/pubmed/24424187.

Faʻalapotopotoga a le Atunuʻu mo faʻafitauli seasea. Eosinophilic fasciitis. rarediseases.org/rare-diseases/eosinophilic-fasciitis/. Faʻafouina 2016. Avanoa ia Mati 6, 2017.