Dermatomyositis

Dermatomyositis o se maso faamai e aofia ai pupuga ma le paʻu mageso. Polymyositis o se tutusa faʻafitauli tulaga, e aofia ai foi maso vaivai, fulafula, agavaivai, ma aano o le tino faʻaleagaina ae leai se paʻu mageso. O vaega ia e lua o se vaega tele o faʻamaʻi e taʻu o le myopathy faʻafefeteina.

Le mafuaʻaga o dermatomyositis e leʻo iloa. Ua manatu tagata popoto atonu e mafua mai i se siama siama o maso poʻo se faʻafitauli i le tino o le tino puipuia. E mafai foi ona tupu i tagata e maua i le kanesa i le manava, mama, po o isi vaega o le tino.

Soʻo se tasi e mafai ona atiaʻe lenei tulaga. E tele taimi e tupu ai i tamaiti tausaga 5 i le 15 ma tagata matutua tausaga 40 i le 60. E aʻafia tele ai fafine nai lo aliʻi.

Faʻailoga e ono aofia ai:

• Musika vaivai, malo, poʻo tiga
• Faafitauli folo
• Lanumoana lanu viole i le mata i luga
• Lanumoana-mumu paʻu mageso
• Manava le mānava

O le vaivai vaivaiga ono tupu faafuasei pe tupu lemu i luga o vaiaso po o masina. Atonu e i ai sau faʻafitauli i le sisii o ou lima i luga o lou ulu, tu i luga mai le nofo ai, ma aʻeaʻe i luga o faasitepu.

Atonu e aliali mai le mageso i ou foliga, tuilima, ua, tauau, pusa i luga, ma tua.

O le fomaʻi soifua maloloina o le a faia se faʻataʻitaʻiga tino. O suʻega e mafai ona aofia ai:

• Toto faʻataʻitaʻi e siaki le maualuga o maso maso na faʻaigoaina o le creatine phosphokinase ma le aldolase
• Toto toto mo faʻamaʻi autoimmune
• ECG
• Electromyography (EMG)
• Maneta resonance imaging (MRI)
• Maso biopsy
• Biopsy o le paʻu
• Isi suʻega suʻega mo le kanesa
• Fatafata x-ray ma le CT faʻataʻitaʻi o le pusa
• Luga gaioiga suʻega
• Folo loloto suesuega
• Myositis faʻapitoa ma fesoʻotaʻi autoantibodies

O le togafitiga autu o le faʻaaogaina o vailaʻau e fai ai le corticosteroid. O le fualaʻau o vailaʻau e lemu lemu tapered ese a maso malosi faʻamalosia. E tusa e 4 i le 6 vaiaso le umi. Oe ono nofo i luga o se maualalo fuala o le corticosteroid vailaʻau mulimuli ane.

O vailaʻau e tineia ai le tino puipuia e mafai ona faʻaaoga e sui ai le vailaʻau. O nei vailaʻau ono aofia ai azathioprine, methotrexate po mycophenolate.

Togafitiga e mafai ona faʻataʻitaʻia pe a o faʻamaʻi e tumau pea le galue e ui lava i nei vailaʻau o:

• Intravenous gamma globulin
• Fualaau faasaina

A faʻamalosia ou maso, e ono taʻu atu e lau tautua ia oe e faifai lemu ona tipi i lalo au tui. Tele o tagata e iai le faʻamaʻi lea e tatau ona inu se vailaʻau e taʻu ole prednisone mo aso o totoe o latou olaga.

Afai o se kanesa ua mafua ai le tulaga, o le maso vaivai ma mageso mafai ona sili atu le lelei pe a aveʻesea le tuma.

Faʻailoga e mafai ona alu ese atoa i nisi tagata, pei o tamaiti.

O le tulaga ono afaina i tagata matutua ona o:

• Ogaoga vaivaiga maso
• Paleni meaai
• Niumonia
• Le manuia le mama

O mafuaʻaga autu o le maliu ma lenei tulaga o kanesa ma mama faʻamaʻi.

Tagata e maua ile faʻamaʻi ole mama ile anti-MDA-5 antibody o loʻo iai se faʻailoga leaga e ui lava ile togafitiga o loʻo iai nei.

Faʻafitauli e ono aofia ai:

• Faamai o le mama
• Ogaoga le afaina o le fatu
• Kanesa (leaga)
• Fula o le fatu
• Tiga soʻoga

Valaʻau lau tautua peʻa iai sau vaivaiga maso poʻo isi faʻailoga o lenei tulaga.

• Dermatomyositis - Gottron papule
• Dermatomyositis - Gottron's papules i luga o le lima
• Dermatomyositis - laumata heliotrope
• Dermatomyositis i luga o vae
• Dermatomyositis - Gottron papule
• Paronychia - faʻamasino
• Dermatomyositis - heliotrope mageso i foliga

Aggarwal R, Rider LG, Ruperto N, et al. 2016 American College of Rheumatology / European League Against Rheumatism Criteria for Minimal, Moderate, and Major Clinical Response in Matutua Dermatomyositis ma Polymyositis: O se International Myositis Iloiloga ma Togafitiga Suʻesuʻega Vaega / Pediatric Rheumatology Faʻataʻitaʻiga Faʻavaomalo Faʻalapotopotoga Fesoasoani Muamua. Gugu Rheumatol. 2017; 69 (5): 898-910. PMID: 28382787 www.ncbi.nlm.nih.gov/pubmed/28382787.

Dalakas MC. Faamaʻi maso maso faamai. N Engl J Med. 2015; 373 (4): 393-394. PMID: 26200989 www.ncbi.nlm.nih.gov/pubmed/26200989.

Nagaraju K, Gladue HS, Lundberg IE. Faamai faʻamaʻi o maso ma isi myopathies. I totonu: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Kelley ma Firestein's Tusitusiga o Rheumatology. 10 ed. Filatelefia, PA: Elsevier; 2017: mata 85.

'Upega Tafaʻilagi a le Atunuʻu mo le Rare Disorder website. Dermatomyositis. rarediseases.org/rare-diseases/dermatomyositis/. Avanoa ia Aperila 1, 2019.