Tusitala: William Ramirez
Aso O Foafoaga: 20 Setema 2021
Faafouga Aso: 19 Setema 2024
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An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Ata: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias e laʻitiiti, faʻalauteleina alatoto i luga ole paʻu. E masani lava e le afaina, ae ono fesoʻotaʻi ma nisi faʻamaʻi.

Telangiectasias ono tupu i soʻo se mea i totonu o le tino. Ae e sili ona faigofie ona vaaia i luga ole paʻu, mucous membranes, ma papaʻe o mata. E masani lava, latou te le mafuaʻaga faʻailoga. O nisi telangiectasias na maligi toto ma mafua ai tele faʻafitauli. Telangiectasias mafai foi ona tupu i le faiʻai poʻo le manava ma mafua ai tele faʻafitauli mai le palapala.

Mafuaʻaga ono aofia ai:

  • Rosacea (paʻu faʻafitauli e mafua ai ona mumu foliga)
  • Matua
  • Faʻafitauli ma genes
  • Maitaga
  • Sailia o le la
  • Vailaʻau vevela
  • Ova le faʻaogaina o vailaʻau vailaʻau
  • Manua i le eria

O faʻamaʻi e fesoʻotaʻi ma lenei tulaga e aofia ai:

  • Ataxia-telangiectasia (faʻamaʻi e aʻafia ai le paʻu, paleni ma faʻamaopoopoina, ma isi vaega o le tino)
  • Fuga o le Bloom (o le maʻi ua maua e mafua ai le pogisa o le tino, paʻu o le paʻu i ultraviolet ave o le la, ma le mumu o foliga)
  • Cutis marmorata telangiectatica congenita (paʻu faʻamaʻi mafua ai pataki o mumu)
  • Fetuunaiga o hemorrhagic telangiectasia (Osler-Weber-Rendu syndrome)
  • Klippel-Trenaunay-Weber syndrome (faʻamaʻi e mafua ai le pisia i le uaina-uaina, alatoto, ma faʻafitauli vaivai o le tino)
  • Nevus flammeus pei o le port-uaina pisia
  • Rosacea (paʻu tulaga e mafua ai mumu o foliga)
  • Sturge-Weber faamaʻi (faʻamaʻi e aofia ai port-uaina pisia ma popolevale faʻafitauli faiga)
  • Xeroderma pigmentosa (faʻamaʻi o le paʻu faʻapea foʻi ma le tino e ufiufi ai le mata e matua nofouta i le ultraviolet malamalama)
  • Lupus (faʻamaʻi o le immune system)
  • CREST syndrome (o se ituaiga o scleroderma e aofia ai le faʻaputuina o maʻila e pei o aano i le paʻu ma isi nofoaga o le tino ma faʻaleagaina sela o loʻo faʻataʻotoina puipui o tamaʻi alatoto)

Valaʻau lau fomaʻi pe a e maitauina le faʻateleina o vaʻa ile paʻu, mucous membranes, poʻo mata.


O le a faʻataunuʻuina le suʻega faʻapitoa ma fesili e uiga i ou faʻailoga, aofia ai:

  • O fea o iai le toto?
  • Na latou maligi toto ma aunoa ma se mafuaaga?
  • O a isi faʻailoga o loʻo iai?

Atonu e manaʻomia ni suʻega e suʻea ai pe faʻafitia ai se tulaga faʻafomaʻi. O suʻega e mafai ona aofia ai:

  • Tofotofoga toto
  • CT suʻega
  • Suʻesuʻe gaioiga galue
  • MRI suʻega
  • X-ray

Sclerotherapy o le togafitiga mo telangiectasias luga o vae. I lenei faiga, o se saline (masima) fofo poʻo isi vailaʻau e tui saʻo i totonu o apogaleveleve uaua i luga o vae. Togafitiga leisa e masani ona faʻaaoga e togafitia ai telangiectasias o foliga.

Ectasias Vascular; Apogaleveleve le angoma

  • Angioma serpiginosum
  • Telangiectasia - vae
  • Telangiectasias - lima i luga

Kelly R, Baker C. Isi vaivaiga faʻaletonu. I: Bolognia JL, Schaffer JV, Cerroni L, eds. Dermatology. 4th ed. Filatelefia, PA: Elsevier; 2018: mata 106.


Patterson JW. Tumua Vascular. I le: Patterson JW, ed. Weedon's Paʻu Faʻasologa. 4th ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: mata 38.

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