Klippel-Trenaunay syndrome

Klippel-Trenaunay syndrome (KTS) o se tulaga seasea lava e masani ona i ai i le taimi o le fanau mai. E masani ona aʻafia le uaina i le uaina, o le tupu tele o ponaivi ma mea vaivai, ma alatoto.

Ole tele o mataupu ole KTS e tutupu e aunoa ma se mafuaʻaga. Ae ui i lea, o nai mataupu e manatu e pasi i lalo i aiga (tofi).

Faʻailoga o le KTS aofia ai:

• Tele faʻamaʻi uaina uafu poʻo isi faʻafitauli toto, aofia ai ma pogisa i le paʻu
• Vailaʻau (e mafai ona vaʻaia i le amataga o lou pepe, ae foliga mai o le a vaʻaia mulimuli ane i le taimi o tamaititi poʻo le talavou)
• Le savali mautu ona o vae-umi eseʻese (aofia vae e umi)
• Ivi, uaua, poʻo tiga neula

Isi faʻailoga mafai:

• Toto mai i le tumutumu
• Toto i le miaga

Tagata ma lenei tulaga ono maua tele tuputupu aʻe o ponaivi ma vaivai vaega. E tupu soo lenei mea i vae, ae e ono afaina ai lima, foliga, ulu, poʻo totoga i totonu.

Eseese faʻataʻitaʻiga faʻataʻitaʻi mafai ona faʻaaogaina e saili ai soʻo se suiga i tino tino ona o lenei tulaga. E fesoasoani foi nei mea i le filifiliga o le fuafuaga o togafitiga. E ono aofia ai:

• MRA
• Endoscopic vevela faʻamamaina togafitiga
• X-ray
• CT scan poʻo le CT venography
• MRI
• Valivali duplex ultrasonography

Ultrasound i le taimi o maitaga ono fesoasoani i le faʻamaoniaina o le tulaga.

O faʻalapotopotoga nei o loʻo tuʻuina mai faʻamatalaga atili e uiga i le KTS:

• Le Klippel-Trenaunay Syndrome Lagolago Vaega - k-t.org
• Vascular Birthmarks Foundation - www.birthmark.org

Tele o tagata e iai le KTS e lelei, e ui lava ole tulaga e ono aʻafia ai latou foliga vaaia. O nisi tagata e i ai faʻafitauli o le mafaufau mai le tulaga.

E iai taimi e mafai ai ona iai ni toto le masani ile manava, e ono manaʻomia ona iloiloina.

Klippel-Trenaunay-Weber syndrome; KTS; Angio-osteohypertrophy; Hemangiectasia hypertrophicans; Nevus verucosus hypertrophicans; Le faʻaletonu ole capillary-lymphatico-venous (CLVM)

Greene AK, Mulliken JB. Vaskal anomalies. I totonu: Rodriguez ED, Losee JE, Neligan PC, eds. Taʻotoga palasitika: Volume 3: Craniofacial, Head and Neck Surgery ma Pediatric Palasitika taotoga. 4th ed. Filatelefia, PA: Elsevier; 2018: mata 39.

'Upega tafaʻilagi K-T Lagolago kulupu. Taʻiala faʻataʻitaʻi ile Klippel-Trenaunaysyndrome (KTS). k-t.org/assets/images/content/BCH-Klippel-Trenaunay-Syndrome-Management-Guidelines-1-6-2016.pdf. Faʻafou Ianuari 6, 2016. Avanoa ia Novema 5, 2019.

Longman RE. Klippel-Trenaunay-Weber syndrome. I le: Copel JA, DʻAlton ME, Feltovich H, et al, eds. Faʻataʻitaʻiga Ata. 2nd ed. Filatelefia, PA: Elsevier; 2018: mata 131.

McCormick AA, Grundwaldt LJ. Vaskal anomalies. I: Zitelli BJ, McIntire SC, Nowalk AJ, eds. Zitelli ma Davis 'Atlas o Pediatric Physical Diagnosis. 7th ed. Filatelefia, PA: Elsevier; 2018: mata 10.